An 8-Year-Old Child with Malignant Deciduoid Mesothelioma of the Abdomen: Report of a Case and Review of the Literature

Pediatric and Development Pathology 2015 April 9 [Epub ahead of print] [Link]

Wolff-Bar M, Dujovny T, Vlodavsky E, Postovsky S, Morgenstern SM, Braslavsky D, Nissan A, Steinberg R, Feinmesser M.

Abstract

Malignant mesothelioma is an uncommon tumor that usually arises in the pleural cavity of adults with a history of asbestos exposure. Less frequently, it appears in the peritoneum or other mesothelial surfaces. Deciduoid mesothelioma is a rare subtype that has been found in both sites. Of the three reported cases in children, two originated in the mesenterium and one in the pleura. We describe a fourth case of pediatric malignant deciduoid mesothelioma, and the third in the mesenteric cavity. The patient was an 8-year-old girl who presented with abdominal pain and fullness. Work-up revealed extensive involvement of the abdomen by a serosa-based tumor. The clinical and pathologic findings are described, and the pertinent literature is reviewed.